This medication is used along with diet changes for long-term treatment of a certain inherited disorder (urea cycle disorder). It helps remove a certain chemical (ammonia) from the body. Too much ammonia in the body can cause brain damage and sometimes death.
This medication should not be used to treat sudden, severely high levels of ammonia in the body. Get medical help right away if you have sudden symptoms of too much ammonia, such as trouble thinking, nausea, vomiting, irritability, trouble speaking, trouble walking, fainting.
How to Use This Medication
Read the Patient Information Leaflet if available from your pharmacist before you start taking this medication and each time you get a refill. If you have any questions, ask your doctor or pharmacist.
Take this medication by mouth or by feeding tube (nasogastric/gastric) exactly as directed by your doctor. The dosage is based on your weight or body size, medical condition, and response to treatment. The total daily dose should be divided into equal amounts and taken with each meal or feeding (such as 4 to 6 times daily). Do not increase or decrease your dose without your doctor's approval.
Carefully measure the dose using a special measuring device/spoon. Take this medication with water, fruit juice, or protein-free infant formula. You may also sprinkle the dose onto a spoonful of solid food (such as mashed potatoes, apple sauce) and eat right away to prevent salty taste. Do not prepare a supply in advance.
If you are using a feeding tube, your health care provider will prepare a liquid mixture of this medication to be given through the feeding tube. Follow your doctor's directions carefully.
Use this medication regularly to get the most benefit from it. To help you remember, take it at the same times each day.